Adverse Drug Reaction Classification System

ADR Ontology
ADR Term Biliary cirrhosis primary
ADR ID BADD_A06934
ADR Hierarchy
09      Hepatobiliary disorders
09.01      Hepatic and hepatobiliary disorders
09.01.04      Hepatic fibrosis and cirrhosis
09.01.04.007      Biliary cirrhosis primary
10      Immune system disorders
10.04      Autoimmune disorders
10.04.09      Hepatic autoimmune disorders
10.04.09.003      Biliary cirrhosis primary
Description FIBROSIS of the hepatic parenchyma due to obstruction of BILE flow (CHOLESTASIS) in the intrahepatic or extrahepatic bile ducts (BILE DUCTS, INTRAHEPATIC; BILE DUCTS, EXTRAHEPATIC). Primary biliary cholangitis involves the destruction of small intra-hepatic bile ducts and bile secretion. Secondary biliary cholangitis is produced by prolonged obstruction of large intrahepatic or extrahepatic bile ducts from a variety of causes. [MeSH]
MedDRA Code 10004661
MeSH ID D008105
ADR Severity Grade (FAERS)
ADR Severity Grade (CTCAE) Not Available
Synonym
Biliary cirrhosis primary | Charcot's cirrhosis | Chronic non-suppurative destructive cholangitis | Hanot's cirrhosis | Hypertrophic cirrhosis | PBC | Primary biliary cirrhosis | Todd's cirrhosis | Liver Cirrhosis, Biliary | Liver Cirrhoses, Biliary | Biliary Cirrhosis | Cirrhosis, Biliary | Secondary Biliary Cholangitis | Biliary Cholangitis, Secondary | Cholangitis, Secondary Biliary | Secondary Biliary Cholangitides | Secondary Biliary Cirrhosis | Cirrhosis, Secondary Biliary | Biliary Cirrhosis, Secondary | Liver Cirrhosis, Obstructive | Obstructive Liver Cirrhosis | Primary Billiary Cholangitis | Billiary Cholangitis, Primary | Cholangitis, Primary Billiary | Primary Billiary Cholangitides | Biliary Cirrhosis, Primary, 1 | Biliary Cirrhosis, Primary | Cholangitis, Chronic Nonsuppurative Destructive | Primary Biliary Cirrhosis
ADR Related Proteins
Protein Name UniProt AC TTD Target ID
Not AvailableNot AvailableNot Available
Drugs Leading to the ADR
Drug IDDrug NameADR Frequency (FAERS)ADR Severity Grade (FAERS)
BADD_D00121Amlodipine0.000031%
BADD_D00142Anastrozole0.000754%
BADD_D00285Bosentan0.000447%
BADD_D00680Dimethyl fumarate0.001834%
BADD_D01835Pregabalin0.000236%
BADD_D02047Sodium oxybate0.001211%
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