Adverse Drug Reaction Classification System

ADR Ontology
ADR Term X-linked lymphoproliferative syndrome
ADR ID BADD_A06511
ADR Hierarchy
01      Blood and lymphatic system disorders
01.13      Haematopoietic neoplasms (excl leukaemias and lymphomas)
01.13.02      Lymphoproliferative disorders NEC (excl leukaemias and lymphomas)
01.13.02.003      X-linked lymphoproliferative syndrome
03      Congenital, familial and genetic disorders
03.17      Immune system disorders congenital
03.17.01      Immune system abnormalities congenital
03.17.01.002      X-linked lymphoproliferative syndrome
10      Immune system disorders
10.03      Immunodeficiency syndromes
10.03.01      Primary immunodeficiency syndromes
10.03.01.003      X-linked lymphoproliferative syndrome
11      Infections and infestations
11.05      Viral infectious disorders
11.05.10      Epstein-Barr viral infections
11.05.10.005      X-linked lymphoproliferative syndrome
16      Neoplasms benign, malignant and unspecified (incl cysts and polyps)
16.21      Haematopoietic neoplasms (excl leukaemias and lymphomas)
16.21.02      Lymphoproliferative disorders NEC (excl leukaemias and lymphomas)
16.21.02.003      X-linked lymphoproliferative syndrome
Description Disorders characterized by proliferation of lymphoid tissue, general or unspecified. [MeSH]
MedDRA Code 10068348
MeSH ID D008232
ADR Severity Grade (FAERS)
ADR Severity Grade (CTCAE) Not Available
Synonym
X-linked lymphoproliferative syndrome | Duncan syndrome | Lymphoproliferative Disorders | Disorder, Lymphoproliferative | Disorders, Lymphoproliferative | Lymphoproliferative Disorder | X-Linked Lymphoproliferative Disorder | Disorder, X-Linked Lymphoproliferative | Disorders, X-Linked Lymphoproliferative | Lymphoproliferative Disorder, X-Linked | Lymphoproliferative Disorders, X-Linked | X Linked Lymphoproliferative Disorder | X-Linked Lymphoproliferative Disorders | Epstein-Barr Virus Infection, Familial Fatal | Epstein Barr Virus Infection, Familial Fatal | Epstein-Barr Virus-Induced Lymphoproliferative Disease In Males | Epstein Barr Virus Induced Lymphoproliferative Disease In Males | Familial Fatal Epstein-Barr Infection | Familial Fatal Epstein Barr Infection | Immunodeficiency 5 | Immunodeficiency 5s | Duncan's Syndrome | Lymphoproliferative Disease, X-Linked | Disease, X-Linked Lymphoproliferative | Diseases, X-Linked Lymphoproliferative | Lymphoproliferative Disease, X Linked | Lymphoproliferative Diseases, X-Linked | X-Linked Lymphoproliferative Diseases | Lymphoproliferative Syndrome, X-Linked, 1 | Purtilo Syndrome | Purtilo Syndromes | Syndrome, Purtilo | Syndromes, Purtilo | X-Linked Lymphoproliferative Disease | X Linked Lymphoproliferative Disease | X-Linked Lymphoproliferative Syndrome | Lymphoproliferative Syndrome, X-Linked | Lymphoproliferative Syndromes, X-Linked | Syndrome, X-Linked Lymphoproliferative | Syndromes, X-Linked Lymphoproliferative | X Linked Lymphoproliferative Syndrome | X-Linked Lymphoproliferative Syndromes | Duncan Disease | Disease, Duncan | Immunodeficiency, X-Linked Progressive Combined Variable | Immunodeficiency, X Linked Progressive Combined Variable
ADR Related Proteins
Protein Name UniProt AC TTD Target ID
Not AvailableNot AvailableNot Available
Drugs Leading to the ADR
Drug IDDrug NameADR Frequency (FAERS)ADR Severity Grade (FAERS)
BADD_D00195Azathioprine--
BADD_D00551Cyclosporine--
BADD_D00858Everolimus--
BADD_D00871Felbamate--
BADD_D00899Fingolimod hydrochloride--
BADD_D00914Fludarabine--
BADD_D00915Fludarabine phosphate--
BADD_D01418Methotrexate--
BADD_D01507Mycophenolate mofetil--
BADD_D01508Mycophenolic acid--
BADD_D01858Propagermanium--
BADD_D02028Sirolimus--
BADD_D02105Tacrolimus--
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