Adverse Drug Reaction Classification System

ADR Ontology
ADR Term Neuromyotonia
ADR ID BADD_A09161
ADR Hierarchy
10      Immune system disorders
10.04      Autoimmune disorders
10.04.05      Muscular autoimmune disorders
10.04.05.008      Neuromyotonia
15      Musculoskeletal and connective tissue disorders
15.05      Muscle disorders
15.05.03      Muscle related signs and symptoms NEC
15.05.03.033      Neuromyotonia
16      Neoplasms benign, malignant and unspecified (incl cysts and polyps)
16.32      Neoplasm related morbidities
16.32.01      Paraneoplastic syndromes NEC
16.32.01.008      Neuromyotonia
17      Nervous system disorders
17.05      Neuromuscular disorders
17.05.03      Neuromuscular disorders NEC
17.05.03.016      Neuromyotonia
Description A rare neuromuscular disorder with onset usually in late childhood or early adulthood, characterized by intermittent or continuous widespread involuntary muscle contractions; FASCICULATION; hyporeflexia; MUSCLE CRAMP; MUSCLE WEAKNESS; HYPERHIDROSIS; TACHYCARDIA; and MYOKYMIA. Involvement of pharyngeal or laryngeal muscles may interfere with speech and breathing. The continuous motor activity persists during sleep and general anesthesia (distinguishing this condition from STIFF-PERSON SYNDROME). Familial and acquired (primarily autoimmune) forms have been reported. (From Ann NY Acad Sci 1998 May 13;841:482-496; Adams et al., Principles of Neurology, 6th ed, p1491) [MeSH]
MedDRA Code 10072359
MeSH ID D020386; D020386; D020386
ADR Severity Grade (FAERS)
ADR Severity Grade (CTCAE) Not Available
Synonym
Neuromyotonia | Isaac's syndrome | Isaacs syndrome | Isaacs Syndrome | Gamstorp-Wohlfart Syndrome | Gamstorp Wohlfart Syndrome | Isaacs' Syndrome | Isaac Syndrome | Myokymia, Myotonia, Muscle Wasting, And Hyperhidrosis | Myokymia, Continuous | Continuous Myokymia | Continuous Myokymias | Myokymias, Continuous | Pseudomyotonia Syndrome of Isaacs | Isaacs Pseudomyotonia Syndrome | Quantal Squander | Syndrome of Continuous Muscle Activity | Continuous Muscle Activity Syndrome | Isaacs-Mertens Syndrome | Isaacs Mertens Syndrome | Acquired Neuromyotonia | Neuromyotonia, Acquired | Pseudomyotonia
ADR Related Proteins
Protein Name UniProt AC TTD Target ID
Not AvailableNot AvailableNot Available
Drugs Leading to the ADR
Drug IDDrug NameADR Frequency (FAERS)ADR Severity Grade (FAERS)
BADD_D00405Ceftriaxone0.030639%
BADD_D01633Oxaliplatin0.001865%
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