Adverse Drug Reaction Classification System

ADR Ontology
ADR Term Dandy-Walker syndrome
ADR ID BADD_A07842
ADR Hierarchy
03      Congenital, familial and genetic disorders
03.10      Neurological disorders congenital
03.10.03      Cerebral disorders congenital
03.10.03.006      Dandy-Walker syndrome
17      Nervous system disorders
17.07      Increased intracranial pressure and hydrocephalus
17.07.01      Hydrocephalic conditions
17.07.01.004      Dandy-Walker syndrome
Description A congenital abnormality of the central nervous system marked by failure of the midline structures of the cerebellum to develop, dilation of the fourth ventricle, and upward displacement of the transverse sinuses, tentorium, and torcula. Clinical features include occipital bossing, progressive head enlargement, bulging of anterior fontanelle, papilledema, ataxia, gait disturbances, nystagmus, and intellectual compromise. (From Menkes, Textbook of Child Neurology, 5th ed, pp294-5) [MeSH]
MedDRA Code 10048411
MeSH ID D003616
ADR Severity Grade (FAERS)
ADR Severity Grade (CTCAE) Not Available
Synonym
Dandy-Walker syndrome | Dandy-Walker Syndrome | Dandy Walker Syndrome | Dandy-Walker Complex | Dandy Walker Complex | Dandy-Walker Complices | Luschka-Magendie Foramina Atresia | Luschka Magendie Foramina Atresia | Dandy-Walker Deformity | Dandy Walker Deformity | Dandy-Walker Deformities | Hydrocephalus, Internal, Dandy-Walker Type | Hydrocephalus, Noncommunicating, Dandy-Walker Type | Dandy-Walker Malformation | Dandy Walker Malformation | Malformation, Dandy-Walker | Dandy-Walker Cyst | Cyst, Dandy-Walker | Cysts, Dandy-Walker | Dandy-Walker Cysts | Dandy-Walker Syndrome, Familial | Dandy Walker Syndrome, Familial | Familial Dandy-Walker Syndrome
ADR Related Proteins
Protein Name UniProt AC TTD Target ID
Not AvailableNot AvailableNot Available
Drugs Leading to the ADR
Drug IDDrug NameADR Frequency (FAERS)ADR Severity Grade (FAERS)
BADD_D00511Clozapine0.005605%
BADD_D01213Isotretinoin0.003157%
BADD_D01265Levetiracetam0.000571%
BADD_D01557Nevirapine0.012155%
BADD_D01627Oseltamivir0.000145%
BADD_D01679Paroxetine0.000187%
BADD_D02010Sertraline0.000121%
BADD_D02373Warfarin0.000180%
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