Adverse Drug Reaction Classification System

ADR Ontology
ADR Term Hairy cell leukaemia
ADR ID BADD_A07270
ADR Hierarchy
01      Blood and lymphatic system disorders
01.10      Leukaemias
01.10.06      Leukaemias chronic lymphocytic
01.10.06.002      Hairy cell leukaemia
16      Neoplasms benign, malignant and unspecified (incl cysts and polyps)
16.01      Leukaemias
16.01.06      Leukaemias chronic lymphocytic
16.01.06.002      Hairy cell leukaemia
Description A neoplastic disease of the lymphoreticular cells which is considered to be a rare type of chronic leukemia; it is characterized by an insidious onset, splenomegaly, anemia, granulocytopenia, thrombocytopenia, little or no lymphadenopathy, and the presence of "hairy" or "flagellated" cells in the blood and bone marrow. [MeSH]
MedDRA Code 10019053
MeSH ID D007943
ADR Severity Grade (FAERS)
ADR Severity Grade (CTCAE) Not Available
Synonym
Hairy cell leukaemia | Hairy cell leukaemia variant | Hairy cell leukemia | Hairy cell leukemia variant | Leukaemic reticuloendotheliosis | Leukemic reticuloendotheliosis | Leukemic reticuloendotheliosis involving intra-abdominal lymph nodes | Leukemic reticuloendotheliosis involving intrapelvic lymph nodes | Leukemic reticuloendotheliosis involving intrathoracic lymph nodes | Leukemic reticuloendotheliosis involving lymph nodes of axilla and upper limb | Leukemic reticuloendotheliosis involving lymph nodes of head, face, and neck | Leukemic reticuloendotheliosis involving lymph nodes of inguinal region and lower limb | Leukemic reticuloendotheliosis involving lymph nodes of multipes sites | Leukemic reticuloendotheliosis involving spleen | Leukemic reticuloendotheliosis, unspecified site, extranodal and solid organ sites | Leukemic reticuloendotheliosis involving lymph nodes of multiple sites | Leukaemic reticuloendotheliosis involving intra-abdominal lymph nodes | Leukaemic reticuloendotheliosis involving intrapelvic lymph nodes | Leukaemic reticuloendotheliosis involving intrathoracic lymph nodes | Leukaemic reticuloendotheliosis involving lymph nodes of axilla and upper limb | Leukaemic reticuloendotheliosis involving lymph nodes of head, face, and neck | Leukaemic reticuloendotheliosis involving lymph nodes of multiples sites | Leukaemic reticuloendotheliosis involving spleen | Leukaemic reticuloendotheliosis involving lymph nodes of multiple sites | Leukemia, Hairy Cell | Leukemic Reticuloendotheliosis | Leukemic Reticuloendothelioses | Reticuloendothelioses, Leukemic | Reticuloendotheliosis, Leukemic | Hairy Cell Leukemia | Hairy Cell Leukemias | Leukemias, Hairy Cell
ADR Related Proteins
Protein Name UniProt AC TTD Target ID
Not AvailableNot AvailableNot Available
Drugs Leading to the ADR
Drug IDDrug NameADR Frequency (FAERS)ADR Severity Grade (FAERS)
BADD_D00479Cladribine0.000730%
BADD_D02160Terbinafine0.001411%
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