Adverse Drug Reaction Classification System

ADR Ontology
ADR Term Haemangioma-thrombocytopenia syndrome
ADR ID BADD_A09997
ADR Hierarchy
01      Blood and lymphatic system disorders
01.08      Platelet disorders
01.08.01      Thrombocytopenias
01.08.01.012      Haemangioma-thrombocytopenia syndrome
16      Neoplasms benign, malignant and unspecified (incl cysts and polyps)
16.02      Miscellaneous and site unspecified neoplasms benign
16.02.01      Cardiovascular neoplasms benign
16.02.01.009      Haemangioma-thrombocytopenia syndrome
23      Skin and subcutaneous tissue disorders
23.06      Skin vascular abnormalities
23.06.04      Skin vascular conditions NEC
23.06.04.007      Haemangioma-thrombocytopenia syndrome
24      Vascular disorders
24.03      Vascular disorders NEC
24.03.03      Vascular malformations and acquired anomalies
24.03.03.049      Haemangioma-thrombocytopenia syndrome
Description Rapidly growing vascular lesion along the midline axis of the neck, upper trunk, and extremities that is characterized by CONSUMPTION COAGULOPATHY; THROMBOCYTOPENIA; and HEMOLYTIC ANEMIA. It is often associated with infantile Kaposiform HEMANGIOENDOTHELIOMA and other vascular tumors such as tufted ANGIOMA. [MeSH]
MedDRA Code 10058423
MeSH ID D059885
ADR Severity Grade (FAERS)
ADR Severity Grade (CTCAE) Not Available
Synonym
Haemangioma-thrombocytopaenia syndrome | Kasabach-Merritt syndrome | Hemangioma-thrombocytopenia syndrome | Haemangioma-thrombocytopenia syndrome | Kasabach-Merritt Syndrome | Kasabach Merritt Syndrome | Syndrome, Kasabach-Merritt | Kasabach-Merritt Phenomenon | Kasabach Merritt Phenomenon | Phenomenon, Kasabach-Merritt | Hemangioma-Thrombocytopenia Syndrome | Hemangioma Thrombocytopenia Syndrome | Hemangioma Thrombocytopenia Syndromes | Syndrome, Hemangioma Thrombocytopenia | Syndromes, Hemangioma Thrombocytopenia | Thrombocytopenia-Hemangioma Syndrome | Syndrome, Thrombocytopenia-Hemangioma | Syndromes, Thrombocytopenia-Hemangioma | Thrombocytopenia Hemangioma Syndrome | Thrombocytopenia-Hemangioma Syndromes
Drugs Leading to the ADR
Drug IDDrug NameADR Frequency (FAERS)ADR Severity Grade (FAERS)
BADD_D01867Propranolol0.000053%
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