Adverse Drug Reaction Classification System

ADR Ontology
ADR Term Primary myelofibrosis
ADR ID BADD_A09342
ADR Hierarchy
01      Blood and lymphatic system disorders
01.13      Haematopoietic neoplasms (excl leukaemias and lymphomas)
01.13.03      Myeloproliferative disorders (excl leukaemias)
01.13.03.008      Primary myelofibrosis
16      Neoplasms benign, malignant and unspecified (incl cysts and polyps)
16.21      Haematopoietic neoplasms (excl leukaemias and lymphomas)
16.21.03      Myeloproliferative disorders (excl leukaemias)
16.21.03.008      Primary myelofibrosis
Description A de novo myeloproliferation arising from an abnormal stem cell. It is characterized by the replacement of bone marrow by fibrous tissue, a process that is mediated by CYTOKINES arising from the abnormal clone. [MeSH]
MedDRA Code 10077161
MeSH ID D055728; D055728; D055728
ADR Severity Grade (FAERS)
ADR Severity Grade (CTCAE) Not Available
Synonym
Primary myelofibrosis | Agnogenic myeloid metaplasia | Primary Myelofibrosis | Myelofibroses, Primary | Myelofibrosis, Primary | Primary Myelofibroses | Bone Marrow Fibrosis | Bone Marrow Fibroses | Fibroses, Bone Marrow | Fibrosis, Bone Marrow | Myelofibrosis | Myelofibroses | Idiopathic Myelofibrosis | Myeloid Metaplasia | Metaplasia, Myeloid | Metaplasias, Myeloid | Myeloid Metaplasias | Myelosclerosis | Myeloscleroses | Myelosis, Nonleukemic | Myeloses, Nonleukemic | Nonleukemic Myeloses | Nonleukemic Myelosis | Chronic Idiopathic Myelofibrosis | Agnogenic Myeloid Metaplasia | Agnogenic Myeloid Metaplasias | Metaplasia, Agnogenic Myeloid | Metaplasias, Agnogenic Myeloid | Myeloid Metaplasia, Agnogenic | Myeloid Metaplasias, Agnogenic | Myelofibrosis With Myeloid Metaplasia
ADR Related Proteins
Protein Name UniProt AC TTD Target ID
Not AvailableNot AvailableNot Available
Drugs Leading to the ADR
Drug IDDrug NameADR Frequency (FAERS)ADR Severity Grade (FAERS)
BADD_D00594Deferasirox0.001521%
BADD_D01110Hydroxyurea0.000417%
BADD_D01978Ruxolitinib0.000556%
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