Adverse Drug Reaction Classification System

ADR Ontology
ADR Term Congenital generalised lipodystrophy
ADR ID BADD_A05272
ADR Hierarchy
03      Congenital, familial and genetic disorders
03.05      Skin and subcutaneous tissue disorders congenital
03.05.01      Skin and subcutaneous tissue disorders congenital NEC
03.05.01.007      Congenital generalised lipodystrophy
05      Endocrine disorders
05.06      Glucose metabolism disorders (incl diabetes mellitus)
05.06.01      Diabetes mellitus (incl subtypes)
05.06.01.011      Congenital generalised lipodystrophy
14      Metabolism and nutrition disorders
14.06      Glucose metabolism disorders (incl diabetes mellitus)
14.06.01      Diabetes mellitus (incl subtypes)
14.06.01.011      Congenital generalised lipodystrophy
23      Skin and subcutaneous tissue disorders
23.07      Skin and subcutaneous tissue disorders NEC
23.07.01      Lipodystrophies
23.07.01.006      Congenital generalised lipodystrophy
Description A type of diabetes mellitus that is characterized by severe INSULIN RESISTANCE and LIPODYSTROPHY. The latter may be generalized, partial, acquired, or congenital (LIPODYSTROPHY, CONGENITAL GENERALIZED). [MeSH]
MedDRA Code 10053547
MeSH ID D003923; D052497
ADR Severity Grade (FAERS) Not Available
ADR Severity Grade (CTCAE) Not Available
Synonym
Congenital lipodystrophy | Lipoatrophic diabetes | Total lipodystrophy | Lipodystrophy congenital | Congenital generalized lipodystrophy | Congenital generalised lipodystrophy | Generalized lipodystrophy | Progressive congenital lipodystrophy | Congenital lipoatrophic diabetes | Berardinelli-Seip syndrome | Generalised lipodystrophy | Diabetes Mellitus, Lipoatrophic | Lipoatrophic Diabetes Mellitus | Lipoatrophic Diabetes | Diabete, Lipoatrophic | Diabetes, Lipoatrophic | Lipoatrophic Diabete
Drugs Leading to the ADR
Drug IDDrug NameADR Frequency (FAERS)ADR Severity Grade (FAERS)
BADD_D01989Saquinavir mesylate--
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