Adverse Drug Reaction Classification System

ADR Ontology
ADR Term Pseudohypoparathyroidism
ADR ID BADD_A03605
ADR Hierarchy
03      Congenital, familial and genetic disorders
03.09      Endocrine disorders congenital
03.09.01      Endocrine disorders congenital NEC
03.09.01.001      Pseudohypoparathyroidism
14      Metabolism and nutrition disorders
14.04      Bone, calcium, magnesium and phosphorus metabolism disorders
14.04.01      Calcium metabolism disorders
14.04.01.008      Pseudohypoparathyroidism
Description A hereditary syndrome clinically similar to HYPOPARATHYROIDISM. It is characterized by HYPOCALCEMIA; HYPERPHOSPHATEMIA; and associated skeletal development impairment and caused by failure of response to PARATHYROID HORMONE rather than deficiencies. A severe form with resistance to multiple hormones is referred to as Type 1a and is associated with maternal mutant allele of the ALPHA CHAIN OF STIMULATORY G PROTEIN. [MeSH]
MedDRA Code 10037126
MeSH ID D011547
ADR Severity Grade (FAERS)
ADR Severity Grade (CTCAE) Not Available
Synonym
Pseudohypoparathyroidism | Pseudohypoparathyroidisms | Pseudohypoparathyroidism, Type Ib | Pseudohypoparathyroidisms, Type Ib | Type Ib Pseudohypoparathyroidism | Type Ib Pseudohypoparathyroidisms | PHD1b | PHD Ib | PHD Ibs | Pseudohypoparathyroidism, Type Ia | Pseudohypoparathyroidisms, Type Ia | Type Ia Pseudohypoparathyroidism | Type Ia Pseudohypoparathyroidisms | Albright Hereditary Osteodystrophy with Multiple Hormone Resistance | PHP Ia
ADR Related Proteins
Protein Name UniProt AC TTD Target ID
Not AvailableNot AvailableNot Available
Drugs Leading to the ADR
Drug IDDrug NameADR Frequency (FAERS)ADR Severity Grade (FAERS)
BADD_D00337Calcitriol--
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