Adverse Drug Reaction Classification System

ADR Ontology
ADR Term Factor XI deficiency
ADR ID BADD_A01605
ADR Hierarchy
01      Blood and lymphatic system disorders
01.01      Coagulopathies and bleeding diatheses (excl thrombocytopenic)
01.01.01      Coagulation factor deficiencies
01.01.01.008      Factor XI deficiency
03      Congenital, familial and genetic disorders
03.15      Blood and lymphatic system disorders congenital
03.15.01      Coagulation disorders congenital
03.15.01.005      Factor XI deficiency
Description A hereditary deficiency of blood coagulation factor XI (also known as plasma thromboplastin antecedent or PTA or antihemophilic factor C) resulting in a systemic blood-clotting defect called hemophilia C or Rosenthal's syndrome, that may resemble classical hemophilia. [MeSH]
MedDRA Code 10016082
MeSH ID D005173
ADR Severity Grade (FAERS)
ADR Severity Grade (CTCAE) Not Available
Synonym
Congenital factor XI deficiency | Factor XI deficiency | Haemophilia C (Factor XI) | Hemophilia C (Factor XI) | Factor XI Deficiency | Deficiency, Factor Eleven | Deficiencies, Factor Eleven | Factor Eleven Deficiencies | Factor 11 Deficiency | Factor Eleven Deficiency | Plasma Thromboplastin Antecedent Deficiency | Hemophilia C | Rosenthal's Syndrome | Rosenthal's Syndromes | Rosenthals Syndrome | Syndrome, Rosenthal's | Rosenthal Syndrome | Rosenthal Syndromes | Syndrome, Rosenthal | Deficiency, Factor 11 | Deficiencies, Factor 11 | Factor 11 Deficiencies | Deficiency, Factor XI | Deficiencies, Factor XI | Factor XI Deficiencies
ADR Related Proteins
Protein Name UniProt AC TTD Target ID
Not AvailableNot AvailableNot Available
Drugs Leading to the ADR
Drug IDDrug NameADR Frequency (FAERS)ADR Severity Grade (FAERS)
BADD_D01989Saquinavir mesylate--
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